Enzyme Replacements/modifiers


Enzyme replacements/modifiers are a crucial category of pharmaceutical active pharmaceutical ingredients (APIs) utilized in the treatment of various enzyme-related disorders. Enzymes play a vital role in the normal functioning of the body by catalyzing specific biochemical reactions. However, in certain medical conditions, the body may lack or produce dysfunctional enzymes, leading to serious health complications.

Enzyme replacement therapy (ERT) involves administering exogenous enzymes to compensate for the enzyme deficiency in patients. These enzymes are typically derived from natural sources or produced using recombinant DNA technology. By introducing these enzymes into the body, they can effectively substitute the missing or defective enzymes, thereby restoring normal metabolic processes.

On the other hand, enzyme modifiers are API substances that regulate the activity of specific enzymes within the body. These modifiers can either enhance or inhibit the enzyme's function, depending on the therapeutic objective. By modulating enzyme activity, these APIs can restore the balance of enzymatic reactions, leading to improved physiological outcomes.

Enzyme replacements/modifiers have shown remarkable success in treating various genetic disorders, such as Gaucher disease, Fabry disease, and lysosomal storage disorders. Additionally, they have demonstrated potential in managing enzyme deficiencies associated with rare diseases and certain types of cancer.

The development and production of enzyme replacements/modifiers involve rigorous research, formulation optimization, and adherence to stringent quality control measures. Pharmaceutical companies invest substantial resources in developing these APIs to ensure their safety, efficacy, and compliance with regulatory standards.

Overall, enzyme replacements/modifiers represent a vital therapeutic category in modern medicine, offering hope and improved quality of life for patients with enzyme-related disorders.

NameCAS numberCategoryAmount of suppliersAPI market price
Abexinostat783355-60-2Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Abivertinib1557267-42-1Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Acifluorfen50594-66-6Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Acotiamide185106-16-5Enzyme Replacements/modifiersView 1 Suppliers Average price per kg: $
Acridine Carboxamide89459-25-6Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Acrizanib1229453-99-9Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Acumapimod836683-15-9Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Alflutinib1869057-83-9Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Alpelisib1217486-61-7Enzyme Replacements/modifiersView 1 Suppliers Average price per kg: $
Aminooxyacetic acid645-88-5Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Anagliptin739366-20-2Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Arachidonyltrifluoromethane149301-79-1Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Ataciguat254877-67-3Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Atreleuton154355-76-7Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Avacopan1346623-17-3Enzyme Replacements/modifiersView 3 Suppliers Average price per kg: $
Avagacestat1146699-66-2Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Avapritinib1703793-34-3Enzyme Replacements/modifiersView 1 Suppliers Average price per kg: $
Avasimibe166518-60-1Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Avidin110539-97-4Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Bafetinib859212-16-1Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Basifungin127785-64-2Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Begacestat769169-27-9Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Belotecan256411-32-2Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Benazeprilat86541-78-8Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Bisindolylmaleimide I133052-90-1Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Bisindolylmaleimide VIII125313-65-7Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Branebrutinib1912445-55-6Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Bromopyruvate1113-59-3Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Buthionine sulfoximine5072-26-4Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Butyrylcholinesterase9001-08-5Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
CP-320626186430-23-9Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Camostat59721-28-7Enzyme Replacements/modifiersView 1 Suppliers Average price per kg: $
Candoxatrilat123122-54-3Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Capmatinib1029712-80-8Enzyme Replacements/modifiersView 1 Suppliers Average price per kg: $
Carbaryl63-25-2Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Cediranib288383-20-0Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Cepeginterferon alfa-2B1192706-52-7Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Chymostatin9076-44-2Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Cilazaprilat90139-06-3Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Ciluprevir300832-84-2Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Coenzyme A85-61-0Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Collagenase clostridium histolyticum9001-12-1Enzyme Replacements/modifiersView 1 Suppliers Average price per kg: $
Coltuximab ravtansine1269764-99-9Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
D-4-hydroxyphenylglycine22818-40-2Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Daglutril182821-27-8Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Danoprevir850876-88-9Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Darapladib356057-34-6Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Darexaban365462-23-3Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Delanzomib847499-27-8Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Delapril83435-66-9Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Deslorelin57773-65-6Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Dichlororibofuranosylbenzimidazole53-85-0Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Difloxacin98106-17-3Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Diphenyleneiodonium244-54-2Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Dipicolinic acid499-83-2Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Dornase alfa143831-71-4Other enzyme replacements/modifiersView 4 Suppliers Average price per kg: $
Dorsomorphin866405-64-3Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Edetate calcium disodium anhydrous62-33-9Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Edetate disodium anhydrous139-33-3Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Elapegademase1709806-75-6Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Eliglustat491833-29-5Other enzyme replacements/modifiersView 8 Suppliers Average price per kg: $
Emodin518-82-1Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Ensartinib1370651-20-9Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Entinostat209783-80-2Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Epicaptopril63250-36-2Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Farudodstat1035688-66-4Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Fedratinib936091-26-8Enzyme Replacements/modifiersView 1 Suppliers Average price per kg: $
Fenthion55-38-9Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Firsocostat1434635-54-7Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Flavin adenine dinucleotide146-14-5Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Flumatinib895519-90-1Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Flumecinol56430-99-0Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Folitixorin3432-99-3Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Fosinoprilat95399-71-6Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Fulacimstat1488354-15-9Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Gedatolisib1197160-78-3Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Hemicellulase9025-56-3Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Huperzine B103548-82-9Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Hyaluronidase488712-31-8Enzyme Replacements/modifiersView 4 Suppliers Average price per kg: $
Ibrexafungerp1207753-03-4Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Ilomastat142880-36-2Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Imetelstat868169-64-6Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Imidapril89371-37-9Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Imidazole288-32-4Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Ipatasertib1001264-89-6Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Isoliquiritigenin961-29-5Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Itanapraced749269-83-8Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Ivacaftor873054-44-5CFTR regulatorView 6 Suppliers Average price per kg: $
Ivosidenib1448347-49-6Enzyme Replacements/modifiersView 1 Suppliers Average price per kg: $
Lanopepden1152107-25-9Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Lavendustin A125697-92-9Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Lazertinib1903008-80-9Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Leupeptin55123-66-5Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Levoketoconazole142128-57-2Enzyme Replacements/modifiersView 1 Suppliers Average price per kg: $
Linrodostat1923833-60-6Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Lometrexol106400-81-1Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Lorlatinib1454846-35-5Enzyme Replacements/modifiersView 1 Suppliers Average price per kg: $
Lorvotuzumab mertansine1008106-64-6Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Lumacaftor936727-05-8CFTR regulatorView 1 Suppliers Average price per kg: $
Lumichrome1086-80-2Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Lumiflavin1088-56-8Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Manitimus202057-76-9Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Melagatran159776-70-2Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Methanesulfonyl Fluoride558-25-8Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Mirodenafil862189-95-5Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Mitemcinal154738-42-8Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Mocetinostat726169-73-9Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Moexiprilat103775-14-0Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Molybdenum7439-98-7Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Molybdenum cofactor872689-63-9Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Momelotinib1056634-68-4Enzyme Replacements/modifiersView 1 Suppliers Average price per kg: $
Motesanib453562-69-1Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
MucopolysaccharidaseEnzyme Replacements/modifiersView 1 Suppliers Average price per kg: $
N(G)-Iminoethylornithine36889-13-1Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
N-omega-nitro-L-arginine methyl ester50903-99-6Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
NADPH53-57-6Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Nadide53-84-9Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Naquotinib1448232-80-1Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Nattokinase133876-92-3Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Nedisertib1637542-33-6Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Nedosiran2266591-83-5Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Nemiralisib1254036-71-9Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Nemonoxacin378746-64-6Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Neopterin2009-64-5Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Nicotinamide adenine dinucleotide phosphate53-59-8Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Nikkomycin Z59456-70-1Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Nirogacestat1290543-63-3Enzyme Replacements/modifiersView 2 Suppliers Average price per kg: $
Obatoclax803712-67-6Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Onvansertib1034616-18-6Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Otamixaban193153-04-7Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Oxetacaine126-27-2Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Ozagrel82571-53-7Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
PD-169316152121-53-4Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Pacritinib937272-79-2Enzyme Replacements/modifiersView 1 Suppliers Average price per kg: $
Pancrelipase53608-75-6Pancreatic enzymesView 1 Suppliers Average price per kg: $
Paxalisib1382979-44-3Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Peficitinib944118-01-8Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Pegvorhyaluronidase alfa1620390-06-8Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Perindoprilat95153-31-4Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Petesicatib1252637-35-6Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Pevonedistat905579-51-3Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Pexidartinib1029044-16-3Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Picric acid88-89-1Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Pipemidic acid51940-44-4Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Piperine94-62-2Enzyme Replacements/modifiersView 1 Suppliers Average price per kg: $
Posiphen116839-68-0Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Pralsetinib2097132-94-8Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Prexasertib1234015-52-1Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Prulifloxacin123447-62-1Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Queuine72496-59-4Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Quinaprilat82768-85-2Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Quinonoid 7,8-Tetrahydrobiopterin79647-29-3Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Racemetyrosine658-48-0Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Ramiprilat87269-97-4Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Ravoxertinib1453848-26-4Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Relebactam1174018-99-5Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Riboflavin tetrabutyrate752-56-7Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Ridaforolimus572924-54-0Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Rigosertib592542-59-1Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Rimacalib215174-50-8Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Rivoceranib811803-05-1Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Ronopterin185243-78-1Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Ropeginterferon alfa-2b1335098-50-4Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Ruboxistaurin169939-94-0Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Rucaparib283173-50-2Enzyme Replacements/modifiersView 2 Suppliers Average price per kg: $
S-Hexylglutathione24425-56-7Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Safinamide133865-89-1Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Safingol15639-50-6Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Sarilumab1189541-98-7Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Selonsertib1448428-04-3Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Selpercatinib2152628-33-4Enzyme Replacements/modifiersView 1 Suppliers Average price per kg: $
Semagacestat425386-60-3Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Serabelisib1268454-23-4Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Sivelestat127373-66-4Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Somapacitan1338578-34-9Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Spebrutinib1202757-89-8Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Stem bromelain37189-34-7Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Subasumstat1858276-04-6Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Tacedinaline112522-64-2Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Talarozole201410-53-9Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Telotristat ethyl1033805-22-9Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Tenalisib1639417-53-0Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Thioctamide940-69-2Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Tilarginine17035-90-4Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Tolrestat82964-04-3Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Tosedostat238750-77-1Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Trandolaprilat87679-71-8Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Trehalose-6-Phosphate4484-88-2Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Ubiquinone Q1727-81-1Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Vactosertib1352608-82-2Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Vatiquinone1213269-98-7Enzyme Replacements/modifiersView 1 Suppliers Average price per kg: $
Vernakalant794466-70-9Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Vesnarinone81840-15-5Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Volixibat1025216-57-2Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Vorolanib1013920-15-4Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Vutrisiran1867157-35-4Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Zanubrutinib1691249-45-2Enzyme Replacements/modifiersView 2 Suppliers Average price per kg: $
Zatolmilast1606974-33-7Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Zenarestat112733-06-9Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
Zopolrestat110703-94-1Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $
p-Hydroxymercuribenzoic acid1126-48-3Enzyme Replacements/modifiersView 0 Suppliers Average price per kg: $